Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics

• Referrals of Suspected CJD Reported to CJD-SS
• CJD Cases Reported to CJD-SS
• CJD Cases Reported by Province
• Incidence of CJD Cases Reported to CJD-SS in Canada

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Referrals of Suspected CJD Reported by CJD-SS¹, 1997-2009² as of April 1, 2009

Year of Reporting	# of Referrals
1997	4
1998	43
1999	63
2000	82
2001	101
2002	103
2003	75
2004	90
2005	96
2006	78
2007	101
2008	100
2009	31
Total Referrals	967

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional

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CJD Deaths Reported by CJD-SS¹, 1994-2007² as of April 1, 2008

Deaths of Definite and Probable CJD
Year	Sporadic	Iatrogenic	Familial	GSS	FFI	vCJD	Total
1994	2	0	0	1	0	0	3
1995	3	0	0	0	0	0	3
1996	13	0	0	0	0	0	13
1997	16	0	1	1	0	0	18
1998	22	1	0	1	0	0	24
1999	26	2	2	1	0	0	31
2000	32	0	0	3	0	0	35
2001	27	0	2	1	0	0	30
2002	31	0	2	2	0	1	36
2003	27	1	1	0	0	0	29
2004	42	0	1	0	0	0	43
2005	40	0	0	2	0	0	42
2006	37	0	1	3	1	0	42
2007	31	0	0	3	0	0	34
2008	32	0	0	0	0	0	32
2009	2	0	0	0	0	0	2
Total	383	4	10	18	1	1	417

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
25 cases included in this table have been preliminarily classified on limited data

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CJD Cases by Province/Territory As of April 1, 2009

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Incidence of CJD Deaths Reported by CJD-SS in Canada As of April 1, 2009

Year of Death	Total CJD Cases	Population of Canada	Incidence Rate
1999	31	30,403,878	1.02
2000	35	30,689,035	1.14
2001	30	31,021,251	0.97
2002¹	36	31,372,587	1.15
2003	29	31,669,150	0.92
2004	43	32,069,999	1.34
2005	42	32,378,122	1.30
2006	42	32,730,213	1.28
2007	34	33,091,228	1.03
2008²	32	33,223,840	0.96
2009²	2	33,331,420	0.06

World Wide average occurrence of CJD is approximately 1-2 per million population

Notes:
¹ As of September 2002, CJD cases include both definite and probable cases of CJD
²Data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
2008 Population Source: http://www.statcan.ca/Daily/English/080625/d080625b.htm
25 cases included in this table have been preliminarily classified on limited data

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National Microbiology Laboratory Genetics and Prion Disease program (HGPD)